A Case Report on Melanotic Neuroectodermal Tumor of Infancy and Review of the Literature

Author Info

Gailann Jugmohansingh Medford S Sharma V Ramsingh C Beharry C Meyers D Banfield R

Corresponding Author

Gailann Jugmohansingh
Department of Otolaryngology, The San Fernando General Hospital, Trinidad and Tobago

A B S T R A C T

Melanotic neuroectodermal tumor of infancy (MNTI) is a rare, benign neoplasm of neural crest origin that most commonly occurs in the first year of life. The craniofacial area is affected 90% of the time with the maxilla being the affected site in the majority of cases. It has a recurrence rate of up to 27% and is associated with malignant transformation in up to 6.5% of patients. The current case describes the clinical presentation and management of a 3-month old male infant with MNTI of the maxilla. Following initial presentation, the tumor grew rapidly to compromise the aerodigestive tract. Surgical resection was performed and the adjacent bone was burred. There has been no clinical recurrence over a 4-year period of follow up.

Article Info

Article Type

Case Report and Review of the Literature

Publication history

Received: Thu 25, Jun 2020
Accepted: Mon 06, Jul 2020
Published: Fri 10, Jul 2020

Copyright

© 2023 Gailann Jugmohansingh. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. Hosting by Science Repository.
DOI: 10.31487/j.AJSCR.2020.03.06