Angiosarcoma Secondary to a Paget’s Disease: A Rare Clinical Case With 5 Years of Follow-Up and Review of the Literature

Author Info

Andrea Di Bernardo Fabio Sciancalepore Fabio L. Giardina M. Silvia Spinelli Matteo G. Lo Duca Primo A. Daolio Stefano Bastoni

Corresponding Author

M. Silvia Spinelli
Orthopaedic Oncology Unit, ASST “Gaetano Pini” - CTO, Milan, Italy

A B S T R A C T

Paget's disease is characterized by disorganized bony tissue due to altered equilibrium of bone formation and resorption. Its malignant transformation is well known and is usually described to an osteosarcoma, often with bad prognosis. In this paper, we present a case clinic of an angiosarcoma from a Paget’s disease of a pelvic bone. The patient underwent a surgical procedure of tumor resection with wide margins (Enneking zone 2-3). The follow-up of 5 years in this case is unique in the literature.

Article Info

Article Type

Case Report and Review of the Literature

Publication history

Received: Mon 11, May 2020
Accepted: Wed 27, May 2020
Published: Thu 04, Jun 2020

Copyright

© 2023 M. Silvia Spinelli. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. Hosting by Science Repository.
DOI: 10.31487/j.CRSS.2020.02.01