Table 1: Presentation, imaging findings and management of previous case reports.

 

Age

Sex

Comorbid

Presentation

Imaging findings

Complications

Management

Pandya VK et al. [1]

34

M

Nil

Bilateral flank pain

US: anechoic PN collections 33mm in width

 

CT: PN collections of density 0-10HU

Nil

Conservative

Chen Z et al. [2]

34

F

Nil

Fever, right flank pain

US: dilatation of right PC space and right PN collection

 

CT: bilateral polycysts in the renal sinus and right PN collection

Nil

Emergency exploratory surgery, followed by nephrectomy for uncontrolled hilar leakage

Choudhury S et al. [3]

16

M

Nil

Abdominal distension, pain

CT: subcapsular PN collections without PC communication, compression of PC system

HTN

Percutaneous drainage and sclerotherapy

Ashraf K et al. [4]

23

F

Para umbilical hernia

Abdominal distension and pain x1/12

US: ascites and bilateral dilatation of PC system

 

CT abdomen: bilateral renal sinus collections 15HU

HTN, ascites

Conservative with diuretics and antihypertensive

Koc NS et al. [5]

30

M

Young HTN

Diagnosed as ADPKD at age 20 based on US kidney findings > MRI done 10y later to calculate kidney volume for tolvaptan treatment

MRI kidneys: multiple peripherally located cysts hyperintense on T2WI and hypointense on T1WI

HTN

Conservative

Umapathy S et al. [6]

49

M

Nil

Left loin pain x1/12

CT: 9 x 6.5 x 6.2 cm cystic lesion in left renal sinus distorting the PC system with PN fat stranding

Renal vein thrombosis

Conservative

Al-Dofri et al. [7]

22

M

Nil

Abdominal distension and pain, dyspnea x6/12

CT: renal sinus cysts 3HU ; PN collection 2HU; right pleural effusion and ascites 3HU

Pleural effusion, ascites

Conservative with diuretics

Pianezza et al. [8]

52

M

Pancreatic psuedocyst

Bilateral flank pain and gross haematuria

US: PN hypoechoic lesions with thin septations, loss of corticomedullary differentiation

 

CT: multilocated pararenal cystic lesion, density of 0-10 HU, atrophic kidney

 

MRI kidneys: non enhancing cystic lesion on T1WI; increased cortical and decreased medullary intensity on T2WI

Gross haematuria

Conservative

Blanc M. et al. [9]

58

M

Newly diagnosed HTN

 

Fatigue

Hb 213g/L

Hct 0.63

US: unilateral right PN anechoic collection with multiple septa

 

CT: water-density right PN collection with lobulated contours extending to the renal hilum with renal parenchymal compression

 

Renal scintigraphy MAG-3: renal function of 47% on the right kidney and 53% on the left

HTN, polycythemia

Percutaneous drainage followed by laparoscopic bilateral marsupialisation

Ali K. et al. [10]

50

F

Lupus nephritis s/p 3 renal transplants

Right lower quadrant pain 13 months following last renal transplant

US: multi-septated thin-walled fluid collection in the hilum separate from collecting system

 

MRI kidney: non enhancing peripelvic multiseptated collection hypointense on T1 hyperintense on T2

Worsening kidney function post-transplant

Percutaneous drainage initially and then wide peritoneal fenestration and omentoplasty

Hamroun A. et al. [11]

34

M

ESRD 2’ FSGS s/p renal transplant

Refractory ascites 10 years following kidney transplant

MR urography: multiple plurilobular fluid collections located at parapyelic, juxtacapsular, and perihilar regions

Inguinoscrotal hydrocele, bladder compression from mass effect

Conversion to mammalian target of rapamycin (mTOR) inhibitor

 

Hydrocele managed conservatively

35

M

ESRD 2’ childhood HUS s/p renal transplant

Chronic pelvic pain with LUTS for 8 years

US: nephromegaly (16
cm), multiple peripyelic cysts, perihepatic, and perisplenic ascites

 

MR urography: nephromegaly (729cc) pericapsular collection and edematous infiltration of perirenal fat

Bladder compression from mass effect resulting in LUTS

Mofetil mycophenolate was switched to mTORi

Dawidek M. T. et al. [12]

55

F

ESRD 2’ microscopic polyangitis s/p renal transplant

New onset ascites 4 years post transplant

US kidneys: loss of corticomedullary differentiation with subcapsular fluid densities

Ascites, umbilical and laparoscopic port incisional hernias

Allograft nephrectomy with concurrent hernia repair

PN: Perinephric; PC: Pelvicalyceal; HU: Hounsfield Units; HTN: Hypertension; Hb: Haemoglobin; Hct: Haematocrit; ESRD: End Stage Renal Disease; FSGS: Focal and Segmental Glomerulosclerosis; HUS: Hemolytic Uraemic Syndrome; LUTS: Lower Urinary Tract Symptoms