Dyskeratosis Congenita: Squamous Cell Carcinoma of the Buccal Mucosa on a Background of Lichen Planus – A Case Report During COVID-19 Pandemic

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Author Info

Khaled Saleh Ben Salah Fatma M. Emaetig Ebrahim H. El Mahjoubi Abdalla O. Jebriel Nada A. Oshah Firas K. Abdulmalik Mohamed A. Elfagieh Wafa A. Baba Mohamed O. Altaweel Naji Zoubia Alla Shoaoba Monir Abdelmollah Yaser O. Howayw Abdouldaim Ukwas Abdulhakim W Zaggut

Corresponding Author

Khaled Saleh Ben Salah
Department of Pathology, National Cancer Institute (NCI), Misrata, Libya

A B S T R A C T

Dyskeratosis Congenita is a severe disorder that involves several systems in the human body and is well-known for its transmission hereditarily through generations. The triad of a) reticular atrophy of the skin with pigmentation b) dystrophy of the nails c) leukoplakia of the oral mucosa characterises this uncommon disorder, which most commonly affects men. One of the key reasons for premature death in this disease is malignant transformation within areas of mucosal hyperkeratosis. In Dyskeratosis Congenita, the simultaneous existence of squamous cell carcinoma (SCC) with lichen planus and or lichenoid reactions in the mucosa of the oral cavity is a rare, stated condition. This report discusses a case of a Libyan male patient affected by Dyskeratosis Congenita that ended with buccal mucosal squamous cell carcinoma developed on a lichen planus background after thirty years of suffering at the age of 64.

Article Info

Article Type

Case Report

Publication history

Received: Fri 02, Apr 2021
Accepted: Tue 20, Apr 2021
Published: Mon 03, May 2021

Copyright

© 2023 Khaled Saleh Ben Salah. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. Hosting by Science Repository.
DOI: 10.31487/j.COR.2021.05.02