Unusual Case of Pseudomyxoma Peritonei of a Mature Teratoma in Adult Men

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Author Info

Cecilia Ceribelli M. Gomes David A. Ayav J. Raft A. Leroux F. Marchal

Corresponding Author

Cecilia Ceribelli
Department of Surgery, Institut de Cancérologie de Lorraine-Alexis Vautrin, Université de Lorraine, Vandoeuvres-lès-Nancy, Nancy, France

A B S T R A C T

Pseudomyxoma peritonei (PMP) is a rare disease usually originating from appendiceal neoplasm and its incidence is 1-2 cases per million. Extra-appendicular origin is less common and is related to ovary, urachus, stomach, colon and pancreas cancer. A few cases of mature ovarian teratoma associated with PMP have been described. We report an extremely rare case of a man treated for a mature teratoma recurrence as a PMP. A 57-year-old man with multiple surgeries for mature teratoma excision as a newborn was addressed to our institution. At the age of 55, a surgical exploration found a low-grade PMP. The patient was asymptomatic, and surveillance was performed. Nine months later, a sub-complete cytoreductive surgery (CRS) with Mitomycin C HIPEC (hyperthermic intraperitoneal chemotherapy) was performed. One year later, the residual mass volume was treated by a new CRS with Mitomycin C HIPEC. After a two-year follow-up patient has no recurrence. PMP extra-appendiceal origin in less than 10%. This is the first reported case of PMP originating as a mature teratoma recurrence in a man. A few cases describe PMP from ovarian teratoma in women. Despite PMP’s different origins, gold standard treatment still remains CRS and HIPEC.

Article Info

Article Type

Case Report

Publication history

Received: Sat 15, Aug 2020
Accepted: Sat 29, Aug 2020
Published: Mon 05, Oct 2020

Copyright

© 2023 Cecilia Ceribelli. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. Hosting by Science Repository.
DOI: 10.31487/j.CRSS.2020.02.04