TY - JOUR
AR - AJSCR-2020-3-106
TI - A Case Report on Melanotic Neuroectodermal Tumor of Infancy and Review of the Literature
AU - Gailann, Jugmohansingh
AU - Medford , S
AU - Sharma , V
AU - Ramsingh , C
AU - Beharry , C
AU - Meyers , D
AU - Banfield , R
JO - American Journal of Surgical Case Reports
PY - 2020
DA - Fri 10, Jul 2020
SN - 2674-5046
DO - http://dx.doi.org/10.31487/j.AJSCR.2020.03.06
UR - https://www.sciencerepository.org/a-case-report-on-melanotic-neuroectodermal-tumor-of-infancy-and_AJSCR-2020-3-106 
KW - Melanotic neuroectodermal tumor of infancy, benign pigmented maxillary mass, neural crest tumor in the head and neck
AB - Melanotic neuroectodermal tumor of infancy (MNTI) is a rare, benign neoplasm of neural crest origin that
most commonly occurs in the first year of life. The craniofacial area is affected 90% of the time with the
maxilla being the affected site in the majority of cases. It has a recurrence rate of up to 27% and is associated
with malignant transformation in up to 6.5% of patients. The current case describes the clinical presentation
and management of a 3-month old male infant with MNTI of the maxilla. Following initial presentation, the
tumor grew rapidly to compromise the aerodigestive tract. Surgical resection was performed and the
adjacent bone was burred. There has been no clinical recurrence over a 4-year period of follow up.