TY - JOUR
AR - IJSCR-2021-1-101
TI - Intra-Abdominal Malignant Solitary Fibrous Tumor with Peritoneal Dissemination: A Case Report
AU - Vivian, Ma
AU - Lawrence , Turner
AU - Robert van , Wiltenburg
AU - Conrad D , Oja
AU - Ananta , Gurung
AU - Shawn, MacKenzie
JO - International Journal of Surgical Case Reports
PY - 2021
DA - Tue 09, Mar 2021
SN - 2674-4171
DO - http://dx.doi.org/10.31487/j.IJSCR.2021.01.01
UR - https://www.sciencerepository.org/intra-abdominal-malignant-solitary-fibrous-tumor-with-peritoneal_IJSCR-2021-1-101 
KW - Solitary fibrous tumor, peritoneal dissemination, intra-abdominal, retroperitoneal sarcoma, malignant solitary fibrous tumor
AB - Solitary fibrous tumor (SFT) is a rare mesenchymal tumor primarily found in the pleura, with occasional presentations in extra-pleural locations. SFTs are typically diagnosed based on compressive symptoms due to their large size. Most SFTs are benign with a low recurrence rate, with an overall good prognosis with an overall 5-year survival of over 90%. Approximately 12-22% of SFTs are malignant and are associated with a higher recurrence rate of up to 78%. Given the low incidence and sparse case series literature, no adjuvant therapies have demonstrated a survival benefit. We present the first case of abdominal malignant SFTs with peritoneal dissemination, describing the presentation, histopathology, treatment planning and surveillance.